Microscopic polyangiitis/polyarteritis: Difference between revisions

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{{ICD10 transition status
{{ICD10 transition status
| OldDxArticle =| CurrentStatus = reconciled  
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| CurrentStatus = reconciled  
| InitialEditorAssigned = Marla Penner
| InitialEditorAssigned = Marla Penner
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{{ICD10 dx
{{ICD10 dx
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| ICD10 Code=M31.7
| ICD10 Code=M31.7
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{{ICD10 category|Heme/immunology}}{{ICD10 category|Cardiovascular}}{{ICD10 category|Vasculitis}}{{ICD10 category|ANCA-associated Vasculitis (AAV)}}


{{ICD10 category|Heme/immunology}}
== Additional Info ==
== Additional Info ==
*Microscopic polyangiitis (MPA) is a vasculitis of small vessels. Patients frequently present with renal manifestations, but systemic manifestations, arthritis, mononeuritis multiplex, and other signs and symptoms are also common.
*Microscopic polyangiitis (MPA) is a vasculitis of small vessels. Patients frequently present with renal manifestations, but systemic manifestations, arthritis, mononeuritis multiplex, and other signs and symptoms are also common.  
*Polyarteritis nodosa (PAN) is a rare disease that results from blood vessel inflammation ("vasculitis") causing injury to organ systems. The areas most commonly affected by PAN include the nerves, intestinal tract, heart, and joints.
*It is considered to be an ANCA-associated Vasculitis (AAV)- '''ANCA Serotype: Primarily associated with P-ANCA, which recognizes myeloperoxidase (MPO).'''
Antineutrophilic cytoplasmic antibody (ANCA) associated vasculitides are a heterogeneous group of rare autoimmune conditions that causes an inflammation of blood vessels with various manifestations. It includes three main diseases, which are granulomatosis with polyangiitis (GPA; formerly known as Wegener granulomatosis), eosinophilic granulomatosis with polyangiitis (EGPA; previously known as Churg-Strauss syndrome), and microscopic polyangiitis (MPA). Other ANCA-associated diseases are drug-induced vasculitis and renal limited vasculitis. The clinical presentations of these subtypes can overlap, making accurate diagnosis challenging.


== Alternate ICD10s to consider coding instead or in addition ==
== Alternate ICD10s to consider coding instead or in addition ==
*[[Polyarteritis nodosa (PAN)]]
*[[Polyarteritis nodosa (PAN)]]
*[[Primary Systemic Vasculitis]]
more specifically:
{{ListICD10Category | categoryName = ANCA-associated Vasculitis (AAV)}}
 
more generally:
{{ListICD10Category | categoryName = Vasculitis}}


== Candidate [[Combined ICD10 codes]] ==
== Candidate [[Combined ICD10 codes]] ==
(put links to likely candidates coded with this one, eg. a cause for a trauma.)
 
== Related CCI Codes ==
 
{{Data Integrity Check List}}


== Related Articles ==
== Related Articles ==
{{Related Articles}}
{{Related Articles}}


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