Urinary system NOS, congenital malformation

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ICD10 Diagnosis
Dx: Urinary system NOS, congenital malformation
ICD10 code: Q64
Pre-ICD10 counterpart: none assigned
Charlson/ALERT Scale: none
APACHE Como Component: none
APACHE Acute Component: none
Start Date:
Stop Date:
External ICD10 Documentation

This diagnosis is a part of ICD10 collection.

  • SMW
    • 2019-01-01
    • 2999-12-31
    • Q64
  • Cargo


  • Categories
  • SMW
  • Cargo


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Additional Info

First and foremost is that you should NOT use this code if the problem is acquired and not congenital.

Urinary system includes:

  • Kidneys
  • Ureter
  • Bladder
  • Urethra

Includes

  • Cystic kidney disease (congenital) that is NOT Polycystic kidney(s)
  • Horseshoe kidney-occurs during fetal development as the kidneys of the fetus rise from the pelvic area, they become attached (“fuse”) together at the lower end or base. By fusing, they form into a U shape, like a horseshoe.
  • Congenital absence of bladder and urethra
  • Congenital absence of kidney (often called solitary kidney)
  • Congenital diverticulum of bladder
  • Congenital posterior urethral valves
  • Epispadias
  • Exstrophy of urinary bladder
  • Malformation of bladder or urethra NOS
  • Malformation of urachus
  • Medullary sponge kidney
  • Other atresia and stenosis of urethra and bladder neck
  • Other congenital malformations of bladder and urethra ie; hernia of bladder
  • Prolapse of bladder
  • Prolapse of urethra
  • Urinary meatus
  • Urethrorectal fistula
  • Pelvic kidney
  • Combine with Chromosomal abnormality, NOS if appropriate

Alternate ICD10s to consider coding instead or in addition

Candidate Combined ICD10 codes

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