Edit ICD10 dx: Wegener's granulomatosis

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{{ICD10 transition status | OldDxArticle = Wegener's Granulomatosis / Granulomatosis with polyangiitis | CurrentStatus = reconciled | InitialEditorAssigned = Marla Penner }} == Additional Info == *Wegener's granulomatosis is the OLD name of this disorder. *The new official name is Granulomatosis with polyangiitis (GPA) *It is an autoimmune vasculitis, which causes inflammation and narrowing/blocking of small and medium-sized vessels. '''ANCA Serotype: Primarily associated with C-ANCA, which recognizes proteinase 3 (PR3).''' *This can occur in any organ(s) but most commonly affects the lungs and kidneys -- which can result in a "pulmonary-renal syndrome". Indeed it, along with '''[[Goodpasture syndrome (hypersensitivity angiitis)]]''' are the two most common specific causes of [[Pulmonary-Renal Syndrome in ICD10 | pulmonary-renal syndrome]]s. *It also is referred to as ANCA-associated vasculitis (AAV). Antineutrophilic cytoplasmic antibody (ANCA) associated vasculitides are a heterogeneous group of rare autoimmune conditions that causes an inflammation of blood vessels with various manifestations. It includes three main diseases, which are granulomatosis with polyangiitis (GPA; formerly known as Wegener granulomatosis), eosinophilic granulomatosis with polyangiitis (EGPA; previously known as Churg-Strauss syndrome), and microscopic polyangiitis (MPA). Other ANCA-associated diseases are drug-induced vasculitis and renal limited vasculitis. The clinical presentations of these subtypes can overlap, making accurate diagnosis challenging. == Alternate ICD10s to consider coding instead or in addition == more specifically: {{ListICD10Category | categoryName = ANCA-associated Vasculitis (AAV)}} more generally: {{ListICD10Category | categoryName = Vasculitis}} == Candidate [[Combined ICD10 codes]] == == Related CCI Codes == {{Data Integrity Check List}} == Related Articles == {{Related Articles}} {{ICD10 footer}} {{EndPlaceHolder}}

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