Wegener's granulomatosis
		
		
		
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| ICD10 Diagnosis | |
| Dx: | Wegener's granulomatosis | 
| ICD10 code: | M31.3 | 
| Pre-ICD10 counterpart: | Wegener's Granulomatosis / Granulomatosis with polyangiitis | 
| Charlson/ALERT Scale: | none | 
| APACHE Como Component: | none | 
| APACHE Acute Component: | none | 
| Start Date: | |
| Stop Date: | |
| Data Dependencies(Reports/Indicators/Data Elements): | No results | 
| External ICD10 Documentation | |
This diagnosis is a part of ICD10 collection.
Additional Info
- Wegener's granulomatosis is the OLD name of this disorder.
- The new official name is Granulomatosis with polyangiitis (GPA)
- It is an autoimmune vasculitis, which causes inflammation and narrowing/blocking of small and medium-sized vessels. ANCA Serotype: Primarily associated with C-ANCA, which recognizes proteinase 3 (PR3).
- This can occur in any organ(s) but most commonly affects the lungs and kidneys -- which can result in a "pulmonary-renal syndrome". Indeed it, along with Goodpasture syndrome (hypersensitivity angiitis) are the two most common specific causes of pulmonary-renal syndromes.
- It also is referred to as ANCA-associated vasculitis (AAV). Antineutrophilic cytoplasmic antibody (ANCA) associated vasculitides are a heterogeneous group of rare autoimmune conditions that causes an inflammation of blood vessels with various manifestations. It includes three main diseases, which are granulomatosis with polyangiitis (GPA; formerly known as Wegener granulomatosis), eosinophilic granulomatosis with polyangiitis (EGPA; previously known as Churg-Strauss syndrome), and microscopic polyangiitis (MPA). Other ANCA-associated diseases are drug-induced vasculitis and renal limited vasculitis. The clinical presentations of these subtypes can overlap, making accurate diagnosis challenging.
Alternate ICD10s to consider coding instead or in addition
more specifically:
| ANCA-associated Vasculitis (AAV) codes: | 
more generally:
Candidate Combined ICD10 codes
Related CCI Codes
Data Integrity Checks (automatic list)
none found
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