Microscopic polyangiitis/polyarteritis: Difference between revisions

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{{ICD10 category|Heme/immunology}}{{ICD10 category|Cardiovascular}}
{{ICD10 category|Heme/immunology}}{{ICD10 category|Cardiovascular}}{{ICD10 category|Vasculitis}}{{ICD10 category|ANCA-associated Vasculitis (AAV)}}


== Additional Info ==
== Additional Info ==
*Microscopic polyangiitis (MPA) is a vasculitis of small vessels. Patients frequently present with renal manifestations, but systemic manifestations, arthritis, mononeuritis multiplex, and other signs and symptoms are also common.
*Microscopic polyangiitis (MPA) is a vasculitis of small vessels. Patients frequently present with renal manifestations, but systemic manifestations, arthritis, mononeuritis multiplex, and other signs and symptoms are also common.
*It is considered to be an ANCA-associated Vasculitis (AAV)- '''ANCA Serotype: Primarily associated with P-ANCA, which recognizes myeloperoxidase (MPO).'''
Antineutrophilic cytoplasmic antibody (ANCA) associated vasculitides are a heterogeneous group of rare autoimmune conditions that causes an inflammation of blood vessels with various manifestations. It includes three main diseases, which are granulomatosis with polyangiitis (GPA; formerly known as Wegener granulomatosis), eosinophilic granulomatosis with polyangiitis (EGPA; previously known as Churg-Strauss syndrome), and microscopic polyangiitis (MPA). Other ANCA-associated diseases are drug-induced vasculitis and renal limited vasculitis.  The clinical presentations of these subtypes can overlap, making accurate diagnosis challenging.


== Alternate ICD10s to consider coding instead or in addition ==
== Alternate ICD10s to consider coding instead or in addition ==
*[[Polyarteritis nodosa (PAN)]]
*[[Polyarteritis nodosa (PAN)]]
*[[Primary Systemic Vasculitis]]
more specifically:
{{ListICD10Category | categoryName = ANCA-associated Vasculitis (AAV)}}
 
more generally:
{{ListICD10Category | categoryName = Vasculitis}}


== Candidate [[Combined ICD10 codes]] ==
== Candidate [[Combined ICD10 codes]] ==


== Related CCI Codes ==
{{Data Integrity Check List}}


== Related Articles ==
== Related Articles ==
{{Related Articles}}
{{Related Articles}}


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