Disorder of the immune system, NOS: Difference between revisions

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== Additional Info ==

Includes:

'''Includes'''

* adult-onset Still'~~s Disease~~

* Antisynthetase syndrome

* ~~antisynthetase~~ syndrome

* Autoimmune disorders/autoimmune diseases

* ~~autoimmune~~ disorders/autoimmune diseases

* Mast cell activation disorder

* ~~mast~~ cell activation disorder

* Multisystem inflammatory syndrome in children (MIS-C) for COVID 19 related link with [[Post COVID-19 condition]]

* ~~multisystem~~ inflammatory syndrome in children (MIS-C) for COVID 19 related link with [[Post COVID-19 condition]]

* Pemphigus vulgaris

* ~~pemphigus~~ vulgaris

* VEXAS syndrome- VEXAS syndrome is an adult-onset autoinflammatory disease primarily affecting males, caused by a somatic mutation of the UBA1 gene in hematopoietic progenitor cells. The name VEXAS is an acronym deriving from the core features of disease:

**V: Vacuoles are often identified in the bone marrow stem cells of patients presenting with VEXAS.

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**A: Patients with VEXAS present with a wide array of Autoinflammatory conditions

**S: The mutations which cause VEXAS are Somatic, meaning that they are acquired throughout life, not inherited, and unable to be passed onto one's offspring.

* Evans syndrome

* IgG4 disease

* Immune dysregulation disorder

* CRS- cytokine release syndrome combine with [[Iatrogenic, complication of medical or surgical care NOS]] and if appropriate in comorbid [[Past history of Chimeric Antigen Receptor T-cell Immunotherapy (CAR-T)|Past history of Chimeric Antigen Receptor T-cell Immunotherapy]]

'''Excludes'''

* Adult-onset Still's Disease [[Inflammatory/immune arthritis, NOS]]

== Alternate ICD10s to consider coding instead or in addition ==

@@ Line 12: / Line 12: @@
 == Additional Info ==
-Includes:
+'''Includes'''
-* adult-onset Still's Disease
+* Antisynthetase syndrome
-* antisynthetase syndrome
+* Autoimmune disorders/autoimmune diseases
-* autoimmune disorders/autoimmune diseases
+* Mast cell activation disorder
-* mast cell activation disorder
+* Multisystem inflammatory syndrome in children (MIS-C) for COVID 19 related link with [[Post COVID-19 condition]]
-* multisystem inflammatory syndrome in children (MIS-C) for COVID 19 related link with [[Post COVID-19 condition]]
+* Pemphigus vulgaris
-* pemphigus vulgaris
 * VEXAS syndrome- VEXAS syndrome is an adult-onset autoinflammatory disease primarily affecting males, caused by a somatic mutation of the UBA1 gene in hematopoietic progenitor cells. The name VEXAS is an acronym deriving from the core features of disease:
 **V: Vacuoles are often identified in the bone marrow stem cells of patients presenting with VEXAS.
@@ Line 25: / Line 24: @@
 **A: Patients with VEXAS present with a wide array of Autoinflammatory conditions
 **S: The mutations which cause VEXAS are Somatic, meaning that they are acquired throughout life, not inherited, and unable to be passed onto one's offspring.
+* Evans syndrome
+* IgG4 disease
+* Immune dysregulation disorder
+* CRS- cytokine release syndrome combine with [[Iatrogenic, complication of medical or surgical care NOS]] and if appropriate in comorbid [[Past history of Chimeric Antigen Receptor T-cell Immunotherapy (CAR-T)|Past history of Chimeric Antigen Receptor T-cell Immunotherapy]]
+'''Excludes'''
+* Adult-onset Still's Disease [[Inflammatory/immune arthritis, NOS]]
 == Alternate ICD10s to consider coding instead or in addition ==