Wegener's granulomatosis: Difference between revisions

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{{ICD10 transition status

| OldDxArticle =Wegener's Granulomatosis ~~-P ANCA+~~| CurrentStatus = ~~freshly automatically generated article~~

| OldDxArticle = Wegener's Granulomatosis / Granulomatosis with polyangiitis

| CurrentStatus = reconciled

| InitialEditorAssigned = Marla Penner

~~| MinimumCombinedCodes =~~

}}

{{ICD10 dx

| MinimumCombinedCodes =

| ICD10 Code=M31.3

| BugRequired=

}}

~~{{ICD10 category|Heme/immunology}}~~

== Additional Info ==

*Wegener's granulomatosis is the OLD name of this disorder.

*The new official name is Granulomatosis with polyangiitis (GPA)

*It is an autoimmune vasculitis, which causes inflammation and narrowing/blocking of small and medium-sized vessels. '''ANCA Serotype: Primarily associated with C-ANCA, which recognizes proteinase 3 (PR3).'''

*This can occur in any organ(s) but most commonly affects the lungs and kidneys -- which can result in a "pulmonary-renal syndrome". Indeed it, along with '''[[Goodpasture syndrome (hypersensitivity angiitis)]]''' are the two most common specific causes of [[Pulmonary-Renal Syndrome in ICD10 | pulmonary-renal syndrome]]s.

*It also is referred to as ANCA-associated vasculitis (AAV). Antineutrophilic cytoplasmic antibody (ANCA) associated vasculitides are a heterogeneous group of rare autoimmune conditions that causes an inflammation of blood vessels with various manifestations. It includes three main diseases, which are granulomatosis with polyangiitis (GPA; formerly known as Wegener granulomatosis), eosinophilic granulomatosis with polyangiitis (EGPA; previously known as Churg-Strauss syndrome), and microscopic polyangiitis (MPA). Other ANCA-associated diseases are drug-induced vasculitis and renal limited vasculitis. The clinical presentations of these subtypes can overlap, making accurate diagnosis challenging.

== Alternate ICD10s to consider coding instead ==

== Alternate ICD10s to consider coding instead or in addition ==

(~~turn these into links to the actual diagnosis articles if possible. For some that might make no sense.~~)

more specifically:

{{ListICD10Category | categoryName = ANCA-associated Vasculitis (AAV)}}

more generally:

== Candidate [[Combined ICD10 codes]] ==

== ~~Candidate [[Combined ICD10 codes]]~~ ==

== Related CCI Codes ==

~~(put links to likely candidates coded with this one, eg. a cause for a trauma.)~~

== Related Articles ==

@@ Line 1: / Line 1: @@
 {{ICD10 transition status
-| OldDxArticle =Wegener's Granulomatosis -P ANCA+| CurrentStatus = freshly automatically generated article
+| OldDxArticle = Wegener's Granulomatosis / Granulomatosis with polyangiitis
+| CurrentStatus = reconciled
 | InitialEditorAssigned = Marla Penner
-| MinimumCombinedCodes =
 }}
 {{ICD10 dx
+| MinimumCombinedCodes =
 | ICD10 Code=M31.3
 | BugRequired=
 }}
+{{ICD10 category|Heme/immunology}}{{ICD10 category|Vasculitis}}{{ICD10 category|ANCA-associated Vasculitis (AAV)}}
-{{ICD10 category|Heme/immunology}}
 == Additional Info ==
+*Wegener's granulomatosis is the OLD name of this disorder.
+*The new official name is Granulomatosis with polyangiitis (GPA)
+*It is an autoimmune vasculitis, which causes inflammation and narrowing/blocking of small and medium-sized vessels. '''ANCA Serotype: Primarily associated with C-ANCA, which recognizes proteinase 3 (PR3).'''
+*This can occur in any organ(s) but most commonly affects the lungs and kidneys -- which can result in a "pulmonary-renal syndrome".  Indeed it, along with '''[[Goodpasture syndrome (hypersensitivity angiitis)]]''' are the two most common specific causes of [[Pulmonary-Renal Syndrome in ICD10 | pulmonary-renal syndrome]]s.
+*It also is referred to as ANCA-associated vasculitis (AAV).  Antineutrophilic cytoplasmic antibody (ANCA) associated vasculitides are a heterogeneous group of rare autoimmune conditions that causes an inflammation of blood vessels with various manifestations. It includes three main diseases, which are granulomatosis with polyangiitis (GPA; formerly known as Wegener granulomatosis), eosinophilic granulomatosis with polyangiitis (EGPA; previously known as Churg-Strauss syndrome), and microscopic polyangiitis (MPA). Other ANCA-associated diseases are drug-induced vasculitis and renal limited vasculitis. The clinical presentations of these subtypes can overlap, making accurate diagnosis challenging.
-== Alternate ICD10s to consider coding instead ==
+== Alternate ICD10s to consider coding instead or in addition ==
-(turn these into links to the actual diagnosis articles if possible. For some that might make no sense.)
+more specifically:
+{{ListICD10Category | categoryName = ANCA-associated Vasculitis (AAV)}}
+more generally:
+{{ListICD10Category | categoryName = Vasculitis}}
+== Candidate [[Combined ICD10 codes]] ==
-== Candidate [[Combined ICD10 codes]] ==
+== Related CCI Codes ==
-(put links to likely candidates coded with this one, eg. a cause for a trauma.)
+{{Data Integrity Check List}}
 == Related Articles ==
 {{Related Articles}}
 {{ICD10 footer}}
 {{EndPlaceHolder}}