Wegener's granulomatosis: Difference between revisions

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 == Additional Info ==
-Wegener's granulomatosis is also known as Granulomatosis with polyangiitis (GPA) or Wegener's Granulomatosis -P ANCA+. It is a rare autoimmune disorder that interrupts blood flow to essential organs by causing vasculitis, or inflammation of the blood vessels
+*Wegener's granulomatosis is the OLD name of this disorder.
+*The new official name is Granulomatosis with polyangiitis (GPA)
+**It also is referred to as ANCA-associated vasculitis.
+*It is an autoimmune vasculitis, which causes inflammation and narrowing/blocking of small and medium-sized vessels.
+**This can occur in any organ(s) but most commonly affects the lungs and kidneys -- which can result in a "pulmonary-renal syndrome".  Indeed it, along with '''[[Goodpasture syndrome (hypersensitivity angiitis)]]''' are the two most common specific causes of pulmonary-renal syndromes.
 == Alternate ICD10s to consider coding instead or in addition ==