Churg-Strauss syndrome (eosinophilic granulomatosis with polyangiitis (EGPA), allergic granulomatous angiitis): Difference between revisions
Jump to navigation
Jump to search
| Line 14: | Line 14: | ||
== Additional Info == | == Additional Info == | ||
*Churg-Strauss syndrome, now also referred to by its medically more accurate term eosinophilic granulomatosis with polyangiitis (EGPA), is a rare systemic vasculitis (inflammation in the wall of blood vessels of the body), predominantly affecting small-sized vessels. '''ANCA Serotype: Can be associated with either P-ANCA (primarily MPO-ANCA) or can be ANCA-negative.''' | *Churg-Strauss syndrome, now also referred to by its medically more accurate term eosinophilic granulomatosis with polyangiitis (EGPA), is a rare systemic vasculitis (inflammation in the wall of blood vessels of the body), predominantly affecting small-sized vessels. '''ANCA Serotype: Can be associated with either P-ANCA (primarily MPO-ANCA) or can be ANCA-negative.''' | ||
*This is considered to be an ANCA-associated Vasculitis (AAV)- Antineutrophilic cytoplasmic antibody (ANCA) associated vasculitides are a heterogeneous group of rare autoimmune conditions that causes an inflammation of blood vessels with various manifestations. It includes three main diseases, which are granulomatosis with polyangiitis (GPA; formerly known as Wegener granulomatosis), eosinophilic granulomatosis with polyangiitis (EGPA; previously known as Churg-Strauss syndrome), and microscopic polyangiitis (MPA). Other ANCA-associated diseases are drug-induced vasculitis and renal limited vasculitis. | *This is considered to be an ANCA-associated Vasculitis (AAV)- Antineutrophilic cytoplasmic antibody (ANCA) associated vasculitides are a heterogeneous group of rare autoimmune conditions that causes an inflammation of blood vessels with various manifestations. It includes three main diseases, which are granulomatosis with polyangiitis (GPA; formerly known as Wegener granulomatosis), eosinophilic granulomatosis with polyangiitis (EGPA; previously known as Churg-Strauss syndrome), and microscopic polyangiitis (MPA). Other ANCA-associated diseases are drug-induced vasculitis and renal limited vasculitis. The clinical presentations of these subtypes can overlap, making accurate diagnosis challenging. | ||
== Alternate ICD10s to consider coding instead or in addition == | == Alternate ICD10s to consider coding instead or in addition == | ||