Disorder of the immune system, NOS: Difference between revisions
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== Additional Info == | == Additional Info == | ||
'''Includes''' | |||
* Adult-onset Still's Disease | |||
* Antisynthetase syndrome | |||
* Autoimmune disorders/autoimmune diseases | |||
* Mast cell activation disorder | |||
* Multisystem inflammatory syndrome in children (MIS-C) for COVID 19 related link with [[Post COVID-19 condition]] | |||
* Pemphigus vulgaris | |||
* VEXAS syndrome- VEXAS syndrome is an adult-onset autoinflammatory disease primarily affecting males, caused by a somatic mutation of the UBA1 gene in hematopoietic progenitor cells. The name VEXAS is an acronym deriving from the core features of disease: | |||
**V: Vacuoles are often identified in the bone marrow stem cells of patients presenting with VEXAS. | |||
**E: The E1 ubiquitin conjugating enzyme encoded by the UBA1 gene is mutated in patients. | |||
**X: The mutated UBA1 gene is located on the X-chromosome and thus the disease is almost exclusively found in individuals with XY chromosomes and thus said to be X-linked. | |||
**A: Patients with VEXAS present with a wide array of Autoinflammatory conditions | |||
**S: The mutations which cause VEXAS are Somatic, meaning that they are acquired throughout life, not inherited, and unable to be passed onto one's offspring. | |||
* Evans syndrome | |||
* IgG4 disease | |||
* Immune dysregulation disorder | |||
== Alternate ICD10s to consider coding instead or in addition == | == Alternate ICD10s to consider coding instead or in addition == | ||
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== Related CCI Codes == | == Related CCI Codes == | ||
{{Data Integrity Check List}} | |||
== Related Articles == | == Related Articles == | ||
{{Related Articles}} | {{Related Articles}} | ||
{{ICD10 footer}} | {{ICD10 footer}} | ||
{{EndPlaceHolder}} | {{EndPlaceHolder}} |
Latest revision as of 10:27, 2024 January 18
ICD10 Diagnosis | |
Dx: | Disorder of the immune system, NOS |
ICD10 code: | D89.9 |
Pre-ICD10 counterpart: | Immunological problems |
Charlson/ALERT Scale: | none |
APACHE Como Component: | none |
APACHE Acute Component: | none |
Start Date: | |
Stop Date: | |
External ICD10 Documentation |
This diagnosis is a part of ICD10 collection.
Additional Info
Includes
- Adult-onset Still's Disease
- Antisynthetase syndrome
- Autoimmune disorders/autoimmune diseases
- Mast cell activation disorder
- Multisystem inflammatory syndrome in children (MIS-C) for COVID 19 related link with Post COVID-19 condition
- Pemphigus vulgaris
- VEXAS syndrome- VEXAS syndrome is an adult-onset autoinflammatory disease primarily affecting males, caused by a somatic mutation of the UBA1 gene in hematopoietic progenitor cells. The name VEXAS is an acronym deriving from the core features of disease:
- V: Vacuoles are often identified in the bone marrow stem cells of patients presenting with VEXAS.
- E: The E1 ubiquitin conjugating enzyme encoded by the UBA1 gene is mutated in patients.
- X: The mutated UBA1 gene is located on the X-chromosome and thus the disease is almost exclusively found in individuals with XY chromosomes and thus said to be X-linked.
- A: Patients with VEXAS present with a wide array of Autoinflammatory conditions
- S: The mutations which cause VEXAS are Somatic, meaning that they are acquired throughout life, not inherited, and unable to be passed onto one's offspring.
- Evans syndrome
- IgG4 disease
- Immune dysregulation disorder
Alternate ICD10s to consider coding instead or in addition
- Immune reconstitution syndrome
- Combined immunodeficiency
- Common variable immunodeficiency (CVID)
- Immunodeficiency state, NOS
- Immunodeficiency due to antibody deficiency or defect, hereditary or acquired
Candidate Combined ICD10 codes
Related CCI Codes
Data Integrity Checks (automatic list)
none found
Related Articles
Show all ICD10 Subcategories