Nephritic syndrome, rapidly progressive
| ICD10 Diagnosis | |
| Dx: | Nephritic syndrome, rapidly progressive |
| ICD10 code: | N01 |
| Pre-ICD10 counterpart: | Acute Glomerulonephritis |
| Charlson/ALERT Scale: | none |
| APACHE Como Component: | none |
| APACHE Acute Component: | 2019-0: Metabolic/Renal NOS, 2019-0: Renal/Metabolic NOS |
| Start Date: | |
| Stop Date: | |
| External ICD10 Documentation | |
This diagnosis is a part of ICD10 collection.
Additional Info
- Rapidly progressive glomerulonephritis (RPGN) is a clinical syndrome manifested by features of glomerular disease in the urinalysis and by progressive loss of renal function over a comparatively short period of time (days to weeks). It is most commonly characterized morphologically by extensive crescent formation
- Nephritic syndrome is a syndrome comprising signs of nephritis, which is kidney disease involving inflammation. It often occurs in the glomerulus, where it is called glomerulonephritis. Glomerulonephritis is characterized by inflammation and thinning of the glomerular basement membrane and the occurrence of small pores in the podocytes of the glomerulus. These pores become large enough to permit both proteins and red blood cells to pass into the urine (yielding proteinuria and hematuria, respectively). The cause of this inflammation can be infectious, autoimmune, or thrombotic. If the cause is known then code it in combination with this code.
- By contrast, nephrotic syndrome is characterized by proteinuria and a constellation of other symptoms that specifically do not include hematuria.
- Nephritic syndrome, like nephrotic syndrome, may involve low level of albumin in the blood due to the protein albumin moving from the blood to the urine.
- a classic cause of GN (especially Nephritic syndrome, rapidly progressive is as an immune after-effect of Strep infection, so-called Post-strep GN). To code this we will add a new code B98, to be called Other specified infectious agents as the cause of diseases classified by other ICD10 code -- this new code, with the appropriate Streptoccus code, is then combined with the appropriate Nephritic syndrome code to get Post-strep GN
- In ICD10 there are no codes specific for glomerulonephritis (GN) -- instead the various forms of that entity are included in the various codes for "Nephritic sydrome"
- Nephritic syndrome represents a class/category of renal diseases that are due to non-infectious inflammation of the glomerulus
- Though non-infectious, a classic cause of GN is immune-mediated and elicited by PRIOR infection by a variety of organisms, though Streptococci is the classic (so-called Post-strep GN) if using this code combine with Other specified infectious agents as the cause of diseases classified by other ICD10 code
- Although often primary, i.e. the etiology is auto-immune, there are numerous other conditions that can cause GNs (e.g. post-infectious which is an immune-mediated problem and not due to the organism itself; in association with other immune disorders such as Lupus and vasculitis; immune consequences of drug use such as iv heroin, others). When the etiology is NOT primary, combine the cause with the appropriate Nephritic syndrome code.
- Regarding the various codes for nephritic syndrome (Nephritic syndrome, acute, Nephritic syndrome, rapidly progressive, Nephritic syndrome, chronic, Nephritic syndrome, NOS)
- They include
- glomerulonephritis
- nephritis
- other inflammatory glomerular diseases
- Don't get confused, another way to classify glomerular diseases is by what they look like under the microscope (e.g. minimal change, membranous, crecentic, etc) -- but in ICD10 these are all included within all the codes for nephritic syndrome.
- They include
- The difference between the various Nephritic syndrome codes is clinical onset and persistence:
- code Nephritic syndrome, rapidly progressive if and only if the primary or renal team label it as "rapidly progressive", as in "Rapidly progressive GN"
- if acute in presentation/onset, but they don't label it as "rapidly progressive", then use Nephritic syndrome, acute
- if stated by the teams to be chronic, then use Nephritic syndrome, chronic
- if nothing is said about it's onset or persistence, then use the wastebasket of Nephritic syndrome, NOS
- Important to distinguish the various Nephritic syndrome codes from Nephrotic syndrome
- a classic cause of GN (especially Nephritic syndrome, rapidly progressive is as an immune after-effect of Strep infection, so-called Post-strep GN). To code this we will add a new code B98, to be called Other specified infectious agents as the cause of diseases classified by other ICD10 code -- this new code, with the appropriate Streptoccus code, is then combined with the appropriate Nephritic syndrome code to get Post-strep GN
Alternate ICD10s to consider coding instead or in addition
| Nephritic syndrome codes: |
Candidate Combined ICD10 codes
Related CCI Codes
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