Malformation/disorder NOS, congenital: Difference between revisions

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== Additional Info ==
== Additional Info ==
includes
'''Includes'''
* [https://en.wikipedia.org/wiki/Noonan_syndrome Noonan syndrome]
* [https://en.wikipedia.org/wiki/Situs_inversus Situs inversus]
* all such malformations which don't have their own ICD10 codes in our system, which includes:
* [https://en.wikipedia.org/wiki/Sturge%E2%80%93Weber_syndrome Sturge-Weber syndrome]
** [https://en.wikipedia.org/wiki/Noonan_syndrome Noonan syndrome]
* [https://en.wikipedia.org/wiki/Alport_syndrome Alport syndrome]
** [https://en.wikipedia.org/wiki/Situs_inversus Situs inversus]
** [https://en.wikipedia.org/wiki/Sturge%E2%80%93Weber_syndrome Sturge-Weber syndrome]
** [https://en.wikipedia.org/wiki/Alport_syndrome Alport syndrome]
** [https://en.wikipedia.org/wiki/VACTERL_association VACTERL]
**[https://pubmed.ncbi.nlm.nih.gov/21108393/ UBE2A deficiency syndrome]
** Cornelia de Lange syndrome
** Prader-Willi Syndrome
** Birt Hogg Dube Syndrome
*If a patient has both a malformation for which our system has a specific code (e.g. [[Down syndrome (trisomy 21)|Down syndrome]]) and one or more malformations which fit here, then list both.
*Combine with [[Chromosomal abnormality, NOS]] if appropriate
 
{{ICD10 Guideline congenital blindness}}


== Alternate ICD10s to consider coding instead or in addition ==
== Alternate ICD10s to consider coding instead or in addition ==
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*[[Atrial septal defect (ASD), congenital]]
*[[Atrial septal defect (ASD), congenital]]
*[[Cardiomyopathy, hypertrophic obstructive (HOCM, IHSS)]]
*[[Cardiomyopathy, hypertrophic obstructive (HOCM, IHSS)]]
*[[Brain, congenital malformation]]
*[[Spinal cord, congenital malformation NOS]]
*[[Nervous system NOS, congenital malformation]]
*[[Eye, congenital malformation]]
*[[Ear or hearing, congenital malformation]]
*[[Face and/or neck, congenital malformation]]
*[[Ventricular septal defect (VSD), congenital]]
*[[Cardiac septum, congenital malformation NOS]]
*[[Pulmonary valve or tricuspid valve, congenital malformation]]
*[[Aortic valve or mitral valve, congenital malformation]]
*[[Great arteries NOS, congenital malformation]]
*[[Circulatory system NOS, congenital malformation]]
*[[Respiratory system, congenital malformation]]
*[[Tongue, mouth or pharynx NOS, congenital malformation]]
*[[Digestive system, congenital malformation]]
*[[Female genitalia (internal or external), congenital malformation]]
*[[Male genital organs NOS, congenital malformation]]
*[[Urinary system NOS, congenital malformation]]
*[[Skeletal and/or muscular system NOS, congenital malformation/deformity]]


== Candidate [[Combined ICD10 codes]] ==
== Candidate [[Combined ICD10 codes]] ==

Latest revision as of 09:48, 2024 March 12

ICD10 Diagnosis
Dx: Malformation/disorder NOS, congenital
ICD10 code: Q89
Pre-ICD10 counterpart: Noonan syndrome
Charlson/ALERT Scale: none
APACHE Como Component: none
APACHE Acute Component: none
Start Date:
Stop Date:
External ICD10 Documentation

This diagnosis is a part of ICD10 collection.

  • SMW
    • 2019-01-01
    • 2999-12-31
    • Q89
  • Cargo


  • Categories
  • SMW
  • Cargo


  • Categories
  • SMW
  • Cargo


  • Categories

Additional Info

Includes


Congenital Blindness

Congenital blindness can occur due to actual eye problems or due to problems with the visual nerves or brain. Thus, for this relatively rare entity, code Combined ICD10 codes of Blindness, both eyes (or if appropriate Blindness, one eye) and Malformation/disorder NOS, congenital.

Alternate ICD10s to consider coding instead or in addition

Candidate Combined ICD10 codes

Related CCI Codes

Data Integrity Checks (automatic list)

none found

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